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Los síntomas empezaron 6 meses atrás con plenitud posprandial y una masa epigástrica indolora con aumento progresivo de tamaño. No tenía antecedentes médicos relevantes. La tomografía axial computarizada de abdomen mostró una voluminosa tumoración (16<span class="elsevierStyleHsp" style=""></span>×<span class="elsevierStyleHsp" style=""></span>9<span class="elsevierStyleHsp" style=""></span>×<span class="elsevierStyleHsp" style=""></span>13<span class="elsevierStyleHsp" style=""></span>cm), sólida, heterogénea, con áreas hipodensas quístico-necróticas y neovascularización de predominio periférico, en flanco derecho y mesogastrio, compatible con una neoplasia de origen mesenquimal (<a class="elsevierStyleCrossRef" href="#fig0005">fig. 1</a>A). El tratamiento consistió en resección quirúrgica completa mediante laparotomía de una voluminosa masa que dependía de la curvatura mayor gástrica realizando también gastrectomía atípica en cuña (<a class="elsevierStyleCrossRef" href="#fig0005">fig. 1</a>B). La histopatología mostró células de tipo fusocelular de bajo grado compatibles morfológicamente con tumor del estroma gastrointestinal (GIST). El estudio inmunohistoquímico descartó el diagnóstico diferencial (tumor fibroso solitario, sarcoma miofibroblástico inflamatorio, leiomiosarcoma, tumor maligno de la vaina tendinosa y pecoma), además fue negativo para gen KIT.</p><elsevierMultimedia ident="fig0005"></elsevierMultimedia><p id="par0010" class="elsevierStylePara elsevierViewall">Los GIST son tumores que afectan al tracto gastrointestinal y se suelen localizar en el estómago e intestino delgado proximal. Se identifican por la mutación en genes del KIT o el PDGFRA. Más del 90% de los GIST son positivos para la mutación del KIT, pero existe una mínima proporción sin mutaciones KIT o PDGFRA, llamados «wild type», como nuestro caso. Los profesionales sanitarios deben tener presente esta enfermedad en el estudio de una masa abdominal.</p></span>" "pdfFichero" => "main.pdf" "tienePdf" => true "fechaRecibido" => "2018-08-26" "fechaAceptado" => "2018-09-17" "multimedia" => array:1 [ 0 => array:6 [ "identificador" => "fig0005" "etiqueta" => "Figura 1" "tipo" => "MULTIMEDIAFIGURA" "mostrarFloat" => true "mostrarDisplay" => false "figura" => array:1 [ 0 => array:4 [ "imagen" => "gr1.jpeg" "Alto" => 750 "Ancho" => 1733 "Tamanyo" => 153651 ] ] ] ] ] "idiomaDefecto" => "es" "url" => "/00142565/0000021900000005/v1_201905300714/S0014256518302492/v1_201905300714/es/main.assets" "Apartado" => array:4 [ "identificador" => "1065" "tipo" => "SECCION" "es" => array:2 [ "titulo" => "Medicina en imágenes" "idiomaDefecto" => true ] "idiomaDefecto" => "es" ] "PDF" => "https://static.elsevier.es/multimedia/00142565/0000021900000005/v1_201905300714/S0014256518302492/v1_201905300714/es/main.pdf?idApp=WRCEE&text.app=https://www.revclinesp.es/" "EPUB" => "https://multimedia.elsevier.es/PublicationsMultimediaV1/item/epub/S0014256518302492?idApp=WRCEE" ]
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